Congenital cystic dilation of the bile duct associated with Laurence-Moon-Biedl-Bardet syndrome

We describe a 26-year-old man in whom the Laurence-Moon-Biedl-Bardet syndrome had been associated with congenital cystic dilations of both the intrahepatic and extrahepatic biliary tract. The fact of the simultaneous occurence of two rare diseases in a single patient suggests the congenital origin of cystic dilation of the biliary tract and the importance of examining for a possible association of anomalies in the alimentary tract with the Laurence-Moon-Biedl-Bardet syndrome.