27例乙型血友病患者Ⅸ因子基因突变研究

采用ＰＣＲ（聚合酶链反应）及ＧＡＷＴＳ（ＧｅｎｏｍｉｃＡｍｐｌｉｆｉｃａｔｉｏｎｗｉｔｈＴｒａｎｓｃｒｉｐｔｓＳｅｑｕｅｎｃｉｎｇ）技术，研究了江苏、湖北、山东、广东、福建、宁夏六省区２７例乙型血友病患者及其家系成员ＦⅨ（九因子）基因各２．２Ｋｂ　ＤＮＡ序列。在２ｌ例中发现２０种不同类型的突变。其中１２种是未曾报道的新突变。３８％的突变发生在ＣｐＧ二核苷致序列上，进一步证实了ＣｐＧ确系突变热点。同时检出６例女性为致病基因携带者。对开展基因产前诊断及优生优育等，具有重要意义。     

A CONSTITUTIVE MODEL FOR ELASTIC-PLASTIC DEFORMATION UNDER CYCLIC MULTIAXIAL STRAINING

Abstract— The yield criterion is interpreted as defining the metric of the stress space. Hydrostatic stresses correspond to null geodesies. The plastic strain increment represents a normal projection of the increment undergone by a certain scalar function (hardening function) which depends only on the distance between stress points. This establishes a flow rule formally equivalent to the Prandtl-Reuss equations. Consideration of un-loading processes leads to the analysis of equivalent paths and to the definition of a generalized length or separation which provides a new representation of kinematic hardening.     

Synthesis and Characterization of Nanosized ZSM-5 Zeolite with Mesoporous Carbon Nanotube as Templates

Preparation of nanocrystalline ZSM-5 has been proven possible with carbon matrix by using confined space synthesis. In combination with the hydrothermal method, by the use of a mesoporous carbon nanotube as the inert support material, ZSM-5 with SiO₂/Al₂O₃ ratios of 100 was successfully synthesized with an average crystal size of 27 nm. Their structures were preliminarily characterized by x-ray power diffraction (XRPD) and infrared spectroscopy (IR), and scanning electron microscopy (SEM), respectively. At the same time, we put forward the mechanism about the confined space synthesis in terms of the results.     

计算机辅助施工放样设计与应用

应用数学理论知识和CAD技术对施工图进行建模,从而获得准确的放样参数指导施工,并结合工程实例对计算机辅助施工放样过程进行了具体的介绍。     

时空效应规律在软土深基坑工程中的运用

阐述了时空效应规律在软土深基坑工程中的运用情况，实践证明，运用时空效应规律，能可靠而合理地利用土体自身在基坑开挖过程中控制土体位移的潜力而达到保护环境的目的。     

GPS接收机多径误差及窄相关性能分析

减少GPS接收机多径干扰的办法是采用特殊天线和在接收机中采取一定的措施。文中针对窄相关技术展开分析。重点分析影响接收机多径误差的因素及窄相关的性能，并给出仿真及分析结果。     

星间激光通信技术进展与趋势

较详细地评述了目前国外卫星间光通信技术研究的现状．根据关键单元技术的进展情况，总结了未来星间光通信系统的发展趋势。     

On the relationship between parity space and approaches to fault detection

Parity space approach and H₂ approach are two important fault detection approaches. This paper studies the relationship between these two approaches, which reveals frequency domain characteristics of the optimal solution of the parity space approach on the one side and provides a numerical solution of the H₂-optimal design of residual generators on the other side.     

An analysis of the electrical conductivity in BaSO4-added Ag2SO4 solid electrolyte system

The compositions (1 −x)Ag₂SO₄−(x)BaSO₄, wherex=0·01 to 0·6, were prepared by slow cooling of the melt. The extent of the solid solubility of Ba²⁺ in Ag₂SO₄ was determined by X-ray powder diffraction and scanning electron microscopy. The bulk conductivity of each sample was obtained using a detailed impedance analysis. The partial substitution of Ba²⁺ results in the enhancement of conductivity in compliance with the classical aliovalent doping theory. A simplistic model based on lattice distortion (expansion) due to partial substitution of Ag⁺ by the bigger Ba²⁺ has been considered to explain enhanced conductivity. Beyond solid-solubility limit (5·27 mole%) the BaSO₄-dispersed Ag₂SO₄ conductivity follows the usual trend seen in binary systems. An increase in conductivity in this case is discussed in the light of interfacial reactions and surface defect chemistry. The maximum conductivity in 20 mole% BaSO₄ dispersed Ag₂SO₄ is due to percolation threshold.