| Chediak-Higashi综合征的骨髓细胞超微结构观察 |
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| 引用本文： | 胡群,阮幼冰. Chediak-Higashi综合征的骨髓细胞超微结构观察[J]. 电子显微学报, 2004, 23(1): 75-76 |
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| 作者姓名： | 胡群 阮幼冰 |
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| 作者单位： | 华中科技大学,同济医学院附属同济医院儿科,湖北,武汉,430030;华中科技大学,同济医学院超微病理研究室,湖北,武汉,430030 |
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| 摘 要： | 应用电镜对两例Chediak-Higashi综合征患儿的骨髓细胞进行了观察。观察结果表明其典型异常改变为胞装内含有许多大小不等电子致密颗粒，多较正常者大．其直径可连正常者的10倍以上。偶见吞噬体．胞策内细胞器变性及大的泡状结构．内含絮状物．电镜的检查对该病的确诊有重要的意义。
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| 关 键 词： | Chediak-Higashi综合征 骨髓 超微结构 |
| 文章编号： | 1000-6281(2004)01-0075-02 |
Ultrastructural observation on the bone marrow cells in Chediak-Higashi syndrome |
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| HU Qun,RUAN You-bing. Ultrastructural observation on the bone marrow cells in Chediak-Higashi syndrome[J]. Journal of Chinese Electron Microscopy Society, 2004, 23(1): 75-76 |
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| Authors: | HU Qun RUAN You-bing |
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| Affiliation: | HU Qun~1,RUAN You-bing~2 |
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| Abstract: | Bone marrow aspiration of 2 Chediak-Higashi syndrome patients were observed under electron microscope. The results showed that there were several electron dense granules in the cytoplasm. The granules usually were bigger than normal lysosome, even 10 times bigger than normal ones. The phagosome, degenerated organelles and big vacuoles-shape with flocculent material were also observed in the cytoplasm of bone marrow cells. Ultrastructural observation is very important in diagnosis of Chediak-Higashi syndrome. |
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| Keywords: | Chediak-Higashi syndrome bone marrow ultrastructure |
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